Dr. Walid Elgaddafi, Benghazi, Libya
PMA is currently understood to be a pediatric brain tumor with a distinctive monomorphous pilomyxoid histological pattern ,a more aggressive behavior than classical PA and is typically located in the hypothalamic/chiasmatic region. On imaging, PMA is typically well circumscribed without surrounding edema, consisting of solid with some cystic components and enhances homogeneously with contrast. Although PMA is a WHO grade II low-grade astrocytoma, it appears to follow a more benign clinical course in the three adult patients reported thus far, in addition to our case.
Intra-operatively, the tumor was totally intra-ventricular, and gross total resection was done, through right transcortical approach (middle frontal gyrus). With a histopathology report confirming the diagnosis of pilomyxoid astrocytoma.
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